Porphyria is actually a group of diseases that can also cause problems outside the skin, but the most common type of porphyria in the skin is called PCT (porphyria cutanea tarda). Blisters appear on the skin on the backs of the hands and forearms, and are most often triggered by sunlight. There may be blood in the blisters. Eventually, there may be sores, thin skin and darker skin. In some pain. In addition, some people also have blisters elsewhere on the body. Some may find that their urine is darker.
The cause is an accumulation of porphyrins in the body. Porphyrins are some of the building blocks of the blood's hemoglobin. Some people have a genetic reason why these chemical processes in the body work worse, while in others it can be triggered by diseases. In particular, disease in the liver (haemochromatosis, hepatitis B and C) and excessive alcohol consumption can trigger porphyria.
A diagnosis is made by a doctor, and blood, urine and faeces samples must be analysed. In Norway, samples are sent to Bergen (NAPOS). The treatment consists of protecting the skin from the sun. Liver disease must be followed up, and some also need tablets. Checks usually take place at a dermatologist or internal medicine.
Our dermatologists help people of all ages, from newborns to the elderly, with everything from simple skin changes to serious conditions.
Our dermatologists help people of all ages, from newborns to the elderly, with everything from simple skin changes to serious conditions.
